Terazosin RepUrposing STudy in ALS (TRUST)

  • Research type

    Research Study

  • Full title

    Terazosin RepUrposing STudy in ALS (TRUST): a pilot study targeting PGK1 with terazosin in ALS patients

  • IRAS ID

    301752

  • Contact name

    Alexander Thompson

  • Contact email

    alexander.thompson@ndcn.ox.ac.uk

  • Sponsor organisation

    University of Oxford / Research Governance, Ethics and Assurance Team

  • Eudract number

    2021-003345-38

  • Duration of Study in the UK

    2 years, 0 months, 1 days

  • Research summary

    Amyotrophic lateral sclerosis (ALS), also known as motor neuron disease (MND), is a neurodegenerative disease in which motor neurons deteriorate leading to progressive weakness. Treatment options are very limited. Laboratory evidence suggests that an enzyme called phosphoglycerate kinase 1 (PGK1) might help to protect motor neurons by increasing their energy availability. The drug terazosin is known to activate PGK1, and researchers at the University of Oxford and University of Edinburgh have shown that terazosin helps motor neuron survival in laboratory models of the disease. Terazosin is a drug that is routinely prescribed to patients either for high blood pressure or for symptoms arising from an enlarged prostate gland in men, where it acts through a different mechanism from PGK1 activation.
    As motor neurons deteriorate in ALS, they release substances that can be measured in body fluids and give an indication of how active the disease is. These are called biomarkers. In this pilot study, we will test whether terazosin treatment significantly lowers the levels of biomarkers in the blood, spinal fluid and urine at intervals over the course of 6 months. We will also monitor clinical measurements of disease progression, such as the ALS Functional Rating Score and the spirometry ‘breathing’ test, which are carried out as part of your routine clinical appointments. If this study shows that terazosin alters biomarker levels, suggesting that it potentially slows the disease process in patients with ALS, it would then make a strong case for a larger-scale clinical trial.

  • REC name

    East Midlands - Leicester Central Research Ethics Committee

  • REC reference

    21/EM/0251

  • Date of REC Opinion

    21 Dec 2021

  • REC opinion

    Further Information Favourable Opinion