Natural History Study of Children with Achondroplasia

  • Research type

    Research Study

  • Full title

    An International, Prospective Registry Investigating the Natural History of Children with Achondroplasia

  • IRAS ID

    244565

  • Contact name

    Christine/P Burren

  • Contact email

    Christine.Burren@UHBristol.nhs.uk

  • Sponsor organisation

    Therachon SAS

  • Clinicaltrials.gov Identifier

    NA, NA

  • Duration of Study in the UK

    5 years, 0 months, 1 days

  • Research summary

    The proposed study involves no drug and is called “natural history study”. Such natural history studies are necessary to gain information about rare diseases like achondroplasia and to track how they progress over time. This understanding will help in the clinical development of drugs and therapies to treat achondroplasia. \n\nIts purpose is to study the characteristics of achondroplasia, its symptoms, and markers of bone growth. The bone growth is detected by the length of the bones; it may also be detected by some special substances in children’s blood called biomarkers that may be related to how a child will grow.\n\nThe study consists of a Screening visit, a Baseline visit, 3-month interval visits, a yearly visit (±3 weeks) and a Final Visit. \n\nChildren’s information (about their diseases, symptoms, complaints, the way they grow), will be collected in a registry at baseline and at every 3-month interval visits, for a maximum of 5 years. \n\nIn addition to the collection of information the children will have a blood test for biomarkers assessments at the Baseline visit and then at each annual visit and measurements of their bodies (height, waist circumference, length of their arms, legs, etc.)\n

  • REC name

    South West - Cornwall & Plymouth Research Ethics Committee

  • REC reference

    18/SW/0159

  • Date of REC Opinion

    23 Jul 2018

  • REC opinion

    Further Information Favourable Opinion