Mortality and Morbidity Outcome in Marfans

  • Research type

    Research Study

  • Full title

    Mortality and morbidity outcomes after aorto-vascular surgery in patients with Marfan Syndrome: A UK experience

  • IRAS ID

    294022

  • Contact name

    Julie Sanders

  • Contact email

    j.sanders@qmul.ac.uk

  • Sponsor organisation

    Queen Mary University of London

  • Clinicaltrials.gov Identifier

    NCT04774172

  • Clinicaltrials.gov Identifier

    NCT04774172, ClinicalTrials.gov ID

  • Duration of Study in the UK

    1 years, 11 months, 30 days

  • Research summary

    Marfan Syndrome (MFS) is a genetic disease affecting the eyes, skeleton, heart and arteries. Despite MFS affecting multiple organ systems, cardiovascular manifestations are the most serious and life threatening. Approximately 80% of adult MFS patients will have a dilated aortic root by age 40 years with aortic aneurysm and dissection the leading causes of morbidity and mortality. Improvement in diagnostics and medical and surgical interventions have increased life expectancy. However, the natural history and the influence of medical or surgical interventions in the UK population are not fully described. Further, the incidence of aortovascular surgery in this patient group is unknown as MFS is not routinely documented in the National Institute of Cardiovascular Outcome Research (NICOR) national cardiac surgery dataset and therefore, there is currently no mechanism for exploring the aortovascular outcomes for this patient group.

    We aim to undertake a 10-year secondary analysis of linked national data (National Institute of Cardiovascular Outcome Research (NICOR), Office of National Statistics (ONS), Hospital Episode Statistics (HES)) to identify the UK incidence and outcome of aorto-vascular surgery in patients with Marfan syndrome (MFS). This includes associated hospital length of stay, mortality and morbidity rates.

    Understanding mortality alongside morbidity will allow us to study further the burdens that the aortovascular manifestations may place on MFS population. It will also allow us to continuously evaluate the efficacy of either the health care system or an implemented intervention in place. Further, these metrics will be useful for the stakeholders to effectively prioritise which complications to tackle and to allocate resources toward as well as proactively manage the potential onset of a health event

  • REC name

    London - South East Research Ethics Committee

  • REC reference

    21/LO/0680

  • Date of REC Opinion

    17 Sep 2021

  • REC opinion

    Favourable Opinion