Molecular genetic analysis of duodenal polyposis in FAP and MAP

  • Research type

    Research Study

  • Full title

    Molecular genetic analysis of duodenal polyposis in the inherited colorectal adenoma and cancer predisposition syndromes (Familial Adenomatous Polyposis and MUTYH-Associated Polyposis)

  • IRAS ID

    158519

  • Contact name

    Laura Thomas

  • Contact email

    laura.e.thomas@swansea.ac.uk

  • Sponsor organisation

    Swansea University

  • Duration of Study in the UK

    10 years, 3 months, 31 days

  • Research summary

    Patients with the inherited colorectal adenoma and cancer predisposition syndromes familial adenomatous polyposis (FAP) and MUTYH associated polyposis (MAP) are also at risk of developing malignant and premalignant lesions in other parts of the gastrointestinal tract, particularly the duodenum. Duodenal cancer has become the most common cause of FAP associated death in patients who have had prophylactic colectomy to prevent colorectal cancer.
    Understanding of the natural history of duodenal polyposis is limited in both FAP and MAP. In FAP, duodenal disease is staged using the Spigelman classification, which can identify those at high risk of developing duodenal cancer. This is done at surveillance upper gastrointestinal endoscopy, recommended from age 25 or 30 years onwards. The natural history of duodenal polyposis in MAP is less well defined than in FAP, as patients who have developed duodenal cancers have done so on a background of no or minimal duodenal disease.
    We aim to determine whether the natural history of duodenal polyposis is the same or different in FAP and MAP and to investigate genetic factors, inherited and somatic, associated with growth and progression of duodenal adenomas to cancer in MAP and FAP.

  • REC name

    Wales REC 1

  • REC reference

    15/WA/0075

  • Date of REC Opinion

    16 Mar 2015

  • REC opinion

    Further Information Favourable Opinion