Long-term outcomes in Hirschprung's disease

  • Research type

    Research Study

  • Full title

    Investigating bowel, urinary, and sexual function alongside quality of life indicators in long-term post-operative patients with Hirschsprung's Disease.

  • IRAS ID

    218074

  • Contact name

    Joseph R Davidson

  • Contact email

    Joseph.davidson@gosh.nhs.uk

  • Sponsor organisation

    GOSH/UCL

  • Duration of Study in the UK

    1 years, 2 months, 1 days

  • Research summary

    Hirschsprung's Disease is a condition that babies are born with where the gut is unable to function properly due to a lack of nerve cells. This is currently treated with an operation to form a stoma (colostomy) in the first days of life, followed by a more definitive operation to remove the portion of the bowel that is affected and joining up to form a continuous tube once more.

    We currently know very little about how patients with Hirschsprung's manage in later life. As with many other paediatric conditions, the transition of care is not usually very straightforward into adult services and problems may arise that we as children's doctors may not be aware of. There is evidence to suggest that bowel function, urinary function and sexual function may all be affected into adulthood in patients undergoing surgery to the large intestine and rectum early in their life.

    We would like to conduct a questionnaire-based study investigating patients who have a diagnosis of Hirschsprung's Disease and who have received surgery at our centre (Great Ormond Street.) We will look at domains of bowel function, urinary and sexual function, and quality of life scores.

  • REC name

    London - Camberwell St Giles Research Ethics Committee

  • REC reference

    17/LO/1692

  • Date of REC Opinion

    24 Nov 2017

  • REC opinion

    Further Information Favourable Opinion