Fancostem-Plerixafor & Filgrastim mobilisation in Fanconi Anaemia

  • Research type

    Research Study

  • Full title

    Phase II clinical trial to evaluate safety and efficacy of mobilisation and collection of CD34+ cells after treatment with plerixafor and filgrastim in patients with Fanconi anaemia for subsequent transduction with a lentiviral vector carrying the FANCA gene and reinfusion into the patient

  • IRAS ID

    167477

  • Contact name

    Adrian Thrasher

  • Contact email

    a.thrasher@ucl.ac.uk

  • Sponsor organisation

    Great Ormond street Hospital NHS foundation trust

  • Eudract number

    2014-004272-29

  • Duration of Study in the UK

    1 years, 11 months, 28 days

  • Research summary

    Fanconi anaemia (FA) is a recessive gene disorder disease (with the exception of FA-B), due to a defects in a number of FA genes. FA is principally characterised by bone marrow failure and increased predisposition to cancer. At birth, a patient's blood count is generally normal, but after 5 to 10 years the bone marrow fails, with the average age of onset of haematological disease being 7 years old. About 80% of patients with FA will develop evidence of bone marrow failure (thrombocytopenia, anaemia) in the first decade of life.

    Currently, there are no medications specifically indicated for FA and allogeneic haematopoietic transplantation (which involves replacing the patient’s bone marrow with that of a healthy donor) is the only treatment that definitely restores the normal function of the bone marrow in patients with FA. The results from identical familial donor transplant procedure have improved in recent years with some centres reaching over 80% survival at 5 years after the procedure.

    Patients are invited to participate in a Phase II clinical trial to evaluate safety and efficacy (effect) of mobilization and collection of CD34+ cells after treatment with plerixafor and filgrastim in patients with Fanconi anaemia. If a sufficient number of cells are collected they will be stored in a liquid nitrogen tank and patients will be considered for gene therapy at a later date.

    In this study, we plan to use two medicines, one named plerixafor and the other filgrastim in the hope that the haematopoetic stem cells can mobilise from the bone marrow and be harvested (collected) from patients with Fanconi Anaemia. What this means is that before any cell collection takes place, the medicines that you will receive will help promote movement of these stem cells into the blood stream (mobilisation) making collection more accessible.

  • REC name

    London - West London & GTAC Research Ethics Committee

  • REC reference

    15/LO/0126

  • Date of REC Opinion

    30 Mar 2015

  • REC opinion

    Further Information Favourable Opinion