CLASS-HLH V1.0

  • Research type

    Research Study

  • Full title

    Using clinical and biological information to investigate the aetiopathogenesis of Hemophagocytic lymphohistiocytosis (HLH)

  • IRAS ID

    333580

  • Contact name

    Jessica Manson

  • Contact email

    jessica.manson@nhs.net

  • Sponsor organisation

    University College London

  • Duration of Study in the UK

    5 years, 0 months, 1 days

  • Research summary

    Hemophagocytic lymphohistiocytosis (HLH) is a rare immune disorder where the body reacts inappropriately to a ‘trigger’, usually an infection. Specialised white blood cells (known as T-cells and macrophages) become over-activated, causing severe inflammation and damage to tissues and organs such as the liver, the spleen and the bone marrow. HLH is a rare disease and it can be difficult to diagnose because many of the symptoms can mimic severe infection or other conditions. Treatment is usually coordinated by a specialist team experienced in treating rare immune disorders. The priority of treatment is to damp down (suppress) the immune system to reduce the over-reaction and lessen the risk of tissue and organ damage. This will often involve courses of corticosteroids and chemotherapy medicines, usually given into a vein (intravenously) in hospital. Understanding of HLH has increased, and the diagnosis and survival rates have improved significantly. However, HLH remains a rapidly progressive disease that is relatively poorly understood. The findings of this study will help healthcare professionals and scientists to better understand HLH. In the future, this will hopefully result in quicker recognition, better diagnostics tools and better treatments for HLH.

  • REC name

    Wales REC 5

  • REC reference

    24/WA/0235

  • Date of REC Opinion

    25 Oct 2024

  • REC opinion

    Further Information Favourable Opinion