Chiari II brain malformation: the role of cerebrospinal fluid

  • Research type

    Research Study

  • Full title

    Chiari II brain malformation: the role of cerebrospinal fluid

  • IRAS ID

    344434

  • Contact name

    Andrew Copp

  • Contact email

    a.copp@ucl.ac.uk

  • Sponsor organisation

    UCL – Great Ormond Street Institute of Child Health

  • Clinicaltrials.gov Identifier

    Z6364106/2024/08/97, UCL Data Protection registration number

  • Duration of Study in the UK

    3 years, 0 months, 0 days

  • Research summary

    Spina bifida is a severe birth defect in which the spinal cord fails to develop normally in the embryo. It is usually thought to mainly affect the lower body, with lack of sensation, inability to walk and poor bladder control. However, problems also occur in the brains of children with spina bifida, leading to frequent learning difficulties – which are much less well understood. Although surgery to close spina bifida in the fetus before birth is now possible and is practised at UCLH and Great Ormond Street Hospital, brain anomalies in spina bifida still occur. This is because they arise very early in embryonic and fetal development before surgery can be performed. Our research aims to understand how these brain defects affect children with spina bifida. In this project, we will test whether the brain fluid’s composition is different in spina bifida. Because the fluid leaks constantly from the open spine, it must be made rapidly and, we suggest, in a ‘less mature’ form than normal. The brain fluid bathes the early nerve cells and affects how they multiply and move to their correct positions. We will compare the composition of brain fluid in children with or without spina bifida. Then, we will grow slices of the developing brain in the lab and expose them to brain fluids of differing compositions to examine the effects on nerve cell properties. Labelling the nerve cells will allow us to monitor how well they develop and whether brain fluid from spina bifida has a detrimental effect. This project will help us understand how brain defects arise in children with spina bifida and provide a starting point for future research that is aimed at correcting the brain fluid composition in early pregnancy to improve outcomes in spina bifida.

  • REC name

    North West - Preston Research Ethics Committee

  • REC reference

    24/NW/0331

  • Date of REC Opinion

    31 Oct 2024

  • REC opinion

    Favourable Opinion